Hereditary gingival fibromatosis (HGF), also known as idiopathic gingival hyperplasia, is a rare condition of gingival overgrowth. HGF is characterized as a . Hereditary, drug-induced, and idiopathic gingival overgrowth have been reported . Hereditary gingival fibromatosis can occur as an isolated. Mutation in SOS1, son-of-sevenless gene, is thought to be responsible for hereditary gingival fibromatosis. This report shows a case of.

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The mandible was relatively thinner in angle region bilaterally. Genetic heterogeneity of gingival fibromatosis on chromosome 2p. Post surgically her facial profile improved dramatically and the patient was satisfied with the gnigival [ Figure 3 ]. This page was last edited on 20 Decemberat The HGF is a rare condition of the gingival tissues characterized by enlargement of free and attached gingivae.

Hereditary gingival fibromatosis: Characteristics and treatment approach

Good aesthetic result was achieved without the recurrence of gingival overgrowth. Abstract Hereditary gingival fibromatosis HGF is a rare condition which manifests itself by an enlarged gingival tissue covering teeth to various extents.

Syndromes of Head and Neck. Disease definition Hereditary gingival fibromatosis HGF is a rare benign, slowly progressive, non-inflammatory fibrous hyperplasia of the maxillary and mandibular gingivae that generally occurs with the eruption of the permanent or more rarely the primary dentition or even at birth. Gingival overgrowth in children: Intraoral examination of maxilla [ Figure 3 ] revealed a gross generalized growth of gingiva completely covering the maxillary teeth extending from right maxillary tuberosity to left tuberosity region.

Case Reports -Case 1. Cephalometric findings showed severe mandibular deficiency and fibeomatosis maxillary excess. Here, a mutation is found in sequencing these 16 genes.

Nil Conflict of Interest: Introduction Hereditary gingival fibromatosis HGF is a rare condition with the prevalence of one per population and equal distribution in sexes [ 1 ].

Performing surgery after eruption of the permanent teeth reduces the rate of recurrence 2. How to cite this article: Routine medical history and physical examination revealed no systemic disease. The patient is planned for surgical removal of lesion by CO 2 laser quadrant gingivectomy. This case study also acknowledged how HGF can be part of a multi-system syndrome associated with disorders such as Zimmermann Laband syndrome ear, nose, bone, and nail defects with hepatosplenomegalyRutherford syndrome microphthalmia, mental retardation, athetosis, and hypopigmentationMurray-Puretic Drescher syndrome and Ramon syndrome.

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Hart, Yingze Zhang, Michael C.

Hereditary gingival fibromatosis: Characteristics and treatment approach

Periodontal and restorative treatment in a patient with familial gingival fibromatosis: Her parents did not reveal any evidence of gingival overgrowth. Footnotes Source of Support: The documents contained in this web site are presented hegeditary information purposes only. In the two cases presented here, the DGJ was going through the physiological process of tooth eruption. The microscopic features of the present case were classic of gingival fibromatosis. The post-operative result was uneventful and the patient appearance improved considerably.

Gingival fibromatosis with hypertrichosis. Teeth pulpdentinenamel. Autosomal dominant gingival fibromatosis Autosomal dominant gingival hyperplasia Hereditary gingival hyperplasia Prevalence: It was suggested to the parents that surgery should be performed with nitrous oxide sedation and local anesthesia, opting for external bevel gingivectomy.

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There was no history of consanguinity. A case of 12 year old female child who presented with generalised severe gingival overgrowth, involving both the arches and covering almost the entire dentition, and had all the teeth remaining invisible within the confinement of gingival tissues.

Case of gingivomatosis or elephantiasis of gingival.

The patient can also experience damage or loss of teeth. The treatment consists of surgical excision of the enlarged tissue; often in a series of gingivectomies, that should be complemented by an effective program of oral hygiene. There may or may not be any evidence of history of HGF in the family nor any usage of taking long-term medicines for any particular disease when it comes to diagnosing HGF.


Hereditary gingival fibromatosis

Cementicle Cementoblastoma Gigantiform Cementoma Eruption cyst Epulis Pyogenic granuloma Congenital epulis Gingival enlargement Gingival cyst of the adult Gingival cyst of the newborn Gingivitis Desquamative Granulomatous Plasma cell Hereditary gingival fibromatosis Hypercementosis Hypocementosis Linear gingival erythema Necrotizing periodontal diseases Acute necrotizing ulcerative gingivitis Pericoronitis Peri-implantitis Fubromatosis abscess Periodontal trauma Periodontitis Aggressive As a manifestation of systemic disease Chronic Perio-endo lesion Teething.

Infobox medical condition Articles contradicting other articles. J Can Dent Assoc. Treatment and long-term follow-up of a patient with hereditary gingival fibromatosis: The post-operative instructions were reinforced and a custom made acrylic stent was placed against the surgical area containing periodontal dressing.

Hereditary gingival fibromatosis

The localized form usually affects the maxillary molar and tuberosity area, particularly on the palatal surface. Additional information Further information on this disease Classification s 2 Gene s 3 Clinical signs and symptoms Publications in PubMed Other website s 0. A Age of the patient: In some cases it glngival only minimal involvement characterized by enlargement of the tuberosity area and buccal gingiva around the mandibular molars; however, in severe form it can involve hededitary maxillary and mandibular gingiva.

She was malnourished and belonged to a very poor family.

The maxillary teeth were not all visible except in right and left posterior region. However, treatment is necessary to maintain a healthy lifestyle.

Epidemiology, pathogenesis, and complications. Oral and maxillofacial pathology K00—K06, K11—K14—, — The presented patient seemed to be a case of nonsyndromic HGF which the isolated nature of the condition was further confirmed by a physician. In the present case the diagnosis of HGF was given based on the family history and clinical examination.